TY - JOUR
T1 - Primary intestinal lymphangiectasia successfully treated with defined formula diet
T2 - Report of a case
AU - Ishida, Itsuko
AU - Matsui, Toshiyuki
AU - Iida, Mitsuo
AU - Lien, Gi-Shih
AU - Nishiyama, Kimie
AU - Nakao, Yuzuru
AU - Kobayashi, Kazuo
AU - Murakami, Sumiharu
AU - Nanbu, Takumi
AU - Fujishima, Masatoshi
PY - 1989
Y1 - 1989
N2 - A 19-year-old female was admitted to our hospital because of fever attacks, intermittent whitish stools and pretibial pitting edema. Laboratory examinations on admission demonstrated the following abnormal findings ; T. P. 3.4 g/dl, absolute lymphocyte count 377/mm3, and 125I-PVP test 5.2%. Duodenal and jejunal endoscopic examinations showed scattered white spots and white villi, from which the biopsy specimens revealed dilated lymphatics in the mucosa. On lymphangiogram, marked tortuosity and irregular dilatation of para-aortic lymphatics were seen. Since underlying causes of lymphangiectasia were not evident, she was diagnosed as having primary intestinal lymphangiectasia, and was treated successfully with a defined formula diet containing medium chain triglyceride, namely, the presenting symptoms, laboratory data and endoscopic findings were markedly improved about 1.5 months after the treatment.
AB - A 19-year-old female was admitted to our hospital because of fever attacks, intermittent whitish stools and pretibial pitting edema. Laboratory examinations on admission demonstrated the following abnormal findings ; T. P. 3.4 g/dl, absolute lymphocyte count 377/mm3, and 125I-PVP test 5.2%. Duodenal and jejunal endoscopic examinations showed scattered white spots and white villi, from which the biopsy specimens revealed dilated lymphatics in the mucosa. On lymphangiogram, marked tortuosity and irregular dilatation of para-aortic lymphatics were seen. Since underlying causes of lymphangiectasia were not evident, she was diagnosed as having primary intestinal lymphangiectasia, and was treated successfully with a defined formula diet containing medium chain triglyceride, namely, the presenting symptoms, laboratory data and endoscopic findings were markedly improved about 1.5 months after the treatment.
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U2 - 10.11280/gee1973b.31.3032
DO - 10.11280/gee1973b.31.3032
M3 - Article
AN - SCOPUS:85004570737
SN - 0387-1207
VL - 31
SP - 3032
EP - 3041
JO - Gastroenterological Endoscopy
JF - Gastroenterological Endoscopy
IS - 11
ER -