Central Retinal Vein Occlusion Secondary to Bonnet-Dechaume-Blanc Syndrome

A 23-year-old woman with Bonnet-Dechaume-Blanc syndrome recognized by arteriovenous malformations in the retina (Fig A) and the right suprasellar region reported an acute onset of blurred vision with visual acuity deteriorating from 20/60 to counting finger at 20 cm. Dilated examination revealed central retinal vein occlusion related to the arteriovenous abnormality (Fig B). Intravitreal implantation of slow-release dexamethasone was performed (Fig C). The diffuse retinal flame-shaped hemorrhages and the vascular tortuosity were reduced (Fig D). The patient recovered her visual acuity to 20/60 without other ocular symptoms at the 3-year follow-up visit.